Case Report

Acquired Chiari I Malformation Secondary to Spontaneous Intracranial Hypotension Syndrome and Persistent Hypoglycemia: A Case Report

10.4274/jcrpe.0042

  • Hasan Önal
  • Atilla Ersen
  • Hakan Gemici
  • Erdal Adal
  • Serhat Güler
  • Serdar Sander
  • Sait Albayram

J Clin Res Pediatr Endocrinol 0;0(0):0-0 [e-Pub] PMID: 29513222

Spontaneous intracranial hypotension (SIH) is a rare and potentially serious condition in childhood. Cerebrospinal fluid (CSF) volume depletion is thought to be the main causative feature for intracranial hypotension, results from spontaneous CSF leak, often at the spine level. SIH is increasingly diagnosed in clinical practice, although it manifests into a variegated symptomatology. Indeed, downward displacement of the brain, sometimes mimicking a Chiari I malformation, but concomitant presentation of these syndromes has rarely been reported. We present herein a case of a SIH with Chiari 1 malformation accompanied with an unusual clinical presentation of persistent hypoglycemia.

Keywords: Intracranial hypotension,hypoglycemia,vagotomy