Early Onset Diabetes in Two Children due to Progeria, a Monogenic Disease of DNA Repair
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Case Report

Early Onset Diabetes in Two Children due to Progeria, a Monogenic Disease of DNA Repair

J Clin Res Pediatr Endocrinol 2020;12(3):315-318 DOI: 10.4274/jcrpe.galenos.2019.2019.0126
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Abstract

Progeria syndrome is a rare disorder in childhood which causes accelerated systemic aging. Due to the accelerated aging process, disorders which normally occur only in old age will appear in these children at a much younger age. We report two children with progeria syndrome, in whom fulminant diabetes mellitus manifested at a very early age.

Keywords: Progeria syndrome, diabetes mellitus, metformin, prevention

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