J Clin Res Pediatr Endocrinol. 2018; 10(4): 391-394 | DOI: 10.4274/jcrpe.0042
Acquired Chiari I Malformation Secondary to Spontaneous Intracranial Hypotension Syndrome and Persistent Hypoglycemia: A Case Report
Hasan Önal1, Atilla Ersen2, Hakan Gemici3, Erdal Adal1, Serhat Güler4, Serdar Sander5, Sait Albayram61University of Health Sciences, Kanuni Sultan Süleyman Training and Research Hospital, Clinic of Pediatric Endocrinology and Metabolism, İstanbul, Turkey
2University of Health Sciences, Okmeydanı Training and Research Hospital, Clinic of Pediatrics, İstanbul, Turkey
3University of Health Sciences, Kanuni Sultan Süleyman Training and Research Hospital, Clinic of Pediatrics, İstanbul, Turkey
4Bezmialem Vakıf University Faculty of Medicine, Department of Pediatric Neurology, İstanbul, Turkey
5University of Health Sciences, Kanuni Sultan Süleyman Training and Research Hospital, Clinic of Pediatric Surgery, İstanbul, Turkey
6İstanbul University Cerrahpaşa Faculty of Medicine, Department of Radiology, İstanbul, Turkey
Spontaneous intracranial hypotension (SIH) is a rare and potentially serious condition in childhood. Cerebrospinal fluid (CSF) volume depletion is thought to be the main causative feature for intracranial hypotension and results from a spontaneous CSF leak, often at the spine level. SIH is increasingly diagnosed in clinical practice, although it manifests a varied symptomatology. The downward displacement of the brain, sometimes mimicking a Chiari I malformation, has rarely been reported. We present a case of a SIH with Chiari I malformation accompanied by an unusual clinical presentation of persistent hypoglycemia.
Keywords: Intracranial hypotension, hypoglycemia, vagotomy
Hasan Önal, Atilla Ersen, Hakan Gemici, Erdal Adal, Serhat Güler, Serdar Sander, Sait Albayram. Acquired Chiari I Malformation Secondary to Spontaneous Intracranial Hypotension Syndrome and Persistent Hypoglycemia: A Case Report. J Clin Res Pediatr Endocrinol. 2018; 10(4): 391-394
Manuscript Language: English