ISSN: 1308-5727 | E-ISSN: 1308-5735
Volume : 7 Issue : 4 Year : 2024
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Abstracting & Indexing
Turkish Society for Pediatric Endocrinology and Diabetes
Inflammatory Myofibroblastic Tumor Presenting with Diabetes Insipidus in an Eight-Year-Old Boy: A Case Report [J Clin Res Pediatr Endocrinol]
J Clin Res Pediatr Endocrinol. 2015; 7(4): 340-343 | DOI: 10.4274/jcrpe.1961

Inflammatory Myofibroblastic Tumor Presenting with Diabetes Insipidus in an Eight-Year-Old Boy: A Case Report

Erkan Sarı1, Erman Ataş2, Engin Burak Bulut3, Sebahattin Sarı4, Onur Akın1, Mehmet Saldır1, Yıldırım Karslıoğlu5, Ediz Yeşilkaya1
1Gülhane Military Medicine Academy, Department Of Pediatric Endocrinology, Ankara, Turkey
2Gülhane Military Medicine Academy, Department Of Pediatric Oncology, Ankara, Turkey
3Gülhane Military Medicine Academy, Department Of Pediatric Surgery, Ankara, Turkey
4Gülhane Military Medicine Academy, Department Of Radiology, Ankara, Turkey
5Gülhane Military Medicine Academy, Department Of Pathology, Ankara, Turkey

Inflammatory myofibroblastic tumors (IMT) develop as a non-neoplastic proliferation of myofibroblasts in a myxoid to collagenous stroma admixed with inflammatory cells. The symptoms depend on the specific location of the tumor, which can be anywhere, but is particularly in the respiratory system. Thus, patients with IMT can present with a variety of findings. A pediatric patient with IMT who presented with cough, breathlessness, polyuria-polydipsia, and convulsions is described in this report.

Keywords: Inflammatory myofibroblastic tumor,diabetes insipidus,child

Erkan Sarı, Erman Ataş, Engin Burak Bulut, Sebahattin Sarı, Onur Akın, Mehmet Saldır, Yıldırım Karslıoğlu, Ediz Yeşilkaya. Inflammatory Myofibroblastic Tumor Presenting with Diabetes Insipidus in an Eight-Year-Old Boy: A Case Report. J Clin Res Pediatr Endocrinol. 2015; 7(4): 340-343
Manuscript Language: English
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